Keywords
Acute fibrinous and organizing pneumonia
Lung disease
Submitted : 2024-06-23
Accepted : 2024-07-08
Published : 2024-07-23
Abstract
Adult-onset Still’s disease (AOSD) is a rare condition that lies between autoinflammatory syndrome and autoimmune disease. The main clinical manifestations include fever, chills, rash, joint swelling and pain, peripheral blood leukocytosis, splenomegaly, etc. It is a systemic disease affecting between 1 and 34 people per million. The average age of onset is 35 years old, with a slightly higher prevalence rate in women. Since AOSD lacks early specific symptoms and signs, non-specialist doctors have limited understanding of the disease, and patients are prone to clinical misdiagnosis, mistreatment, and delayed disease progression. This paper reports a patient whose AOSD was misdiagnosed as acute fibrinous and organizing pneumonia.
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