Keywords
Lens dislocation
Psychological care
Home care
Submitted : 2022-12-31
Accepted : 2023-01-15
Published : 2023-01-30
Abstract
Marfan syndrome is a rare genetic disease, and the condition of most patients deteriorates with age. The lesions are mainly cardiovascular, skeletal, and ocular lesions. Its clinical manifestations are characterized by congenital heart disease, ectopic lens, slender body, slender limbs, spider fingers (toes), and general muscle dysplasia. In the early stage of this disease, when the symptoms are not yet clearly manifested, some patients came to the hospital for treatment due to decreased vision. According to the particularity of crystal dislocation patients with Marfan syndrome, this article provides home nursing education in terms of physiological and psychological aspects, and builds an effective home nursing model to promote the physical and mental recovery of patients.
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